Clear cell sarcoma
Clear cell sarcoma
Definition
A rare malignant neoplasm with melanocytic differentiation characterized by the presence of polygonal or spindle shaped clear cells. This sarcoma usually affects the tendons and aponeuroses and is associated with a poor prognosis due to recurrences and metastases.
Also known as chordoid sarcoma, clear cell sarcoma - not kidney, clear cell sarcoma (morphologic abnormality), clear cell sarcoma of soft parts, clear cell sarcoma of soft tissue, clear cell sarcoma/malignant melanoma of soft parts (excluding clear cell sarcoma of the kidney), malignant melanoma of the soft parts, melanoma, malignant, of soft parts — per MONDO