Orbit alveolar rhabdomyosarcoma

Orbit alveolar rhabdomyosarcoma

Definition

A malignant mesenchymal neoplasm that arises in the orbit. It is characterized by the presence of round cells with myoblastic differentiation and a fibrovascular stroma.

Also known as alveolar rhabdomyosarcoma of orbit, alveolar rhabdomyosarcoma of the orbit — per MONDO

Also identified as

Affected Organs

Organ Involvement Source
Craniocervical region Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Craniocervical region Disease Has Primary Anatomic Site NCIT · CC BY 4.0
Muscle tissue Disease Has Primary Anatomic Site NCIT · CC BY 4.0
Musculature Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Musculoskeletal system Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Orbit of skull Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Orbit of skull Disease Has Primary Anatomic Site NCIT · CC BY 4.0
Skeletal muscle Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Skeletal muscle Disease Has Primary Anatomic Site NCIT · CC BY 4.0
Striated muscle tissue Disease Has Primary Anatomic Site NCIT · CC BY 4.0