Medulloepithelioma
Medulloepithelioma
Definition
A rare, usually aggressive malignant embryonal neoplasm of the central nervous system occurring in children. It is characterized by the presence of neuroepithelial cells which form papillary, trabecular, or tubular structures and absence of C19MC amplification. Symptoms include headache, nausea, and vomiting.
Also known as central nervous system medulloepithelioma, medulloepithelioma NOS (morphologic abnormality), medulloepithelioma of the central nervous system, medulloepithelioma, central nervous system — per MONDO
Also identified as
- DOID 4790 per MONDO
- NCIT C4327 per MONDO
- Orphanet 251883 per MONDO
- SCTID 715903004 per MONDO
- UMLS C5231013 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Central nervous system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Central nervous system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Nervous system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |