Hereditary Wilms tumor
Hereditary Wilms tumor
Definition
Familial embryonal neoplasm derived from nephrogenic blastemal cells. Several lines of differentiation, including blastemal, stromal and epithelial, are usually expressed. Comprises approximately 1% of Wilms tumors. (AFIP fascicle version 2.0)
Also known as familial Wilms tumor, familial Wilms tumour, familial Wilms' tumor, familial Wilms' tumour, hereditary kidney adenosarcoma, hereditary nephroblastoma, hereditary renal adenosarcoma, hereditary Wilms tumor — per MONDO
Also identified as
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Adult mammalian kidney | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Adult mammalian kidney | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Genitourinary system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Renal system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Upper urinary tract | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |