Retinal hemangioblastoma
Retinal hemangioblastoma
Definition
A hemangioblastoma that arises from the retina. It is typically a sign of von Hippel-Lindau disease. It may also be seen as an isolated entity without systemic involvement.
Also known as hemangioblastoma of vasculature of retina, retinal capillary hemangioblastoma, retinal hemangioblastoma, vasculature of retina hemangioblastoma — per MONDO
Also identified as
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Blood vessel | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Camera-type eye | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Cardiovascular system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Central nervous system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Central nervous system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Nervous system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Retina | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Retina | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |