Extrahepatic bile duct leiomyosarcoma

Extrahepatic bile duct leiomyosarcoma

Definition

An aggressive malignant smooth muscle neoplasm, arising from an extrahepatic bile duct. It is characterized by a proliferation of neoplastic spindle cells.

Also known as bile duct leiomyosarcoma, extrahepatic bile duct leiomyosarcoma, leiomyosarcoma of bile duct, leiomyosarcoma of extrahepatic bile duct, leiomyosarcoma of the bile duct, leiomyosarcoma of the extrahepatic bile duct — per MONDO

Also identified as

Affected Organs

Organ Involvement Source
Alimentary part of gastrointestinal system Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Alimentary part of gastrointestinal system Disease Has Primary Anatomic Site NCIT · CC BY 4.0
Bile ducts Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Biliary system Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Extrahepatic bile duct Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Extrahepatic bile duct Disease Has Primary Anatomic Site NCIT · CC BY 4.0
Muscle tissue Disease Has Primary Anatomic Site NCIT · CC BY 4.0
Musculature Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Musculoskeletal system Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Smooth muscle Disease Has Primary Anatomic Site NCIT · CC BY 4.0