Hereditary papillary renal cell carcinoma
Hereditary papillary renal cell carcinoma
Definition
A familial carcinoma inherited in an autosomal dominant trait. It is characterized by the development of multiple, bilateral papillary renal cell carcinomas. The carcinomas range from microscopic lesions to clinically symptomatic tumors. It is associated with activating mutations of the MET oncogene.
Also known as familial renal papillary carcinoma, hereditary kidney papillary carcinoma, hereditary papillary carcinoma of kidney, hereditary papillary carcinoma of the kidney, hereditary papillary renal carcinoma, hereditary papillary renal cell cancer, hereditary papillary renal cell carcinoma, renal cell carcinoma, papillary, renal cell carcinoma, papillary, 1, familial and somatic — per MONDO
Also identified as
- DOID 6163 per MONDO
- NCIT C9222 per MONDO
- OMIM 605074 per MONDO
- Orphanet 47044 per MONDO
- SCTID 715561008 per MONDO
- UMLS C0879257 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Adult mammalian kidney | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Adult mammalian kidney | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Genitourinary system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Genitourinary system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Nephron tubule | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Renal system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Renal system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Upper urinary tract | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |