Hereditary kidney oncocytoma

Hereditary kidney oncocytoma

Definition

An inherited condition characterized by the development of kidney oncocytomas which are often bilateral and multifocal. This condition may be connected to Birt-Hogg-Dube syndrome.

Also known as familial renal oncocytoma, hereditary kidney oncocytoma, hereditary renal oncocytoma — per MONDO

Also identified as

Affected Organs

Organ Involvement Source
Adult mammalian kidney Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Adult mammalian kidney Disease Has Primary Anatomic Site NCIT · CC BY 4.0
Genitourinary system Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Genitourinary system Disease Has Primary Anatomic Site NCIT · CC BY 4.0
Renal system Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Renal system Disease Has Primary Anatomic Site NCIT · CC BY 4.0
Upper urinary tract Disease Has Associated Anatomic Site NCIT · CC BY 4.0