Diffuse meningeal melanocytosis

Diffuse meningeal melanocytosis

Definition

A diffuse or multifocal proliferation of uniform nevoid polygonal cells in the leptomeninges. Cells may spread into the Virchow-Robin spaces without frank invasion of the brain. Diffuse melanocytosis carries a poor prognosis even in the absence of histologic malignancy. (WHO)

Also known as diffuse melanocytosis, diffuse melanocytosis (morphologic abnormality), diffuse melanosis, meningeal melanocytosis — per MONDO

Also identified as

Affected Organs

Organ Involvement Source
Central nervous system Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Central nervous system Disease Has Primary Anatomic Site NCIT · CC BY 4.0
Leptomeninx Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Meninx Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Meninx Disease Has Primary Anatomic Site NCIT · CC BY 4.0
Nervous system Disease Has Associated Anatomic Site NCIT · CC BY 4.0