Childhood botryoid rhabdomyosarcoma

Childhood botryoid rhabdomyosarcoma

Definition

A morphologic variant of embryonal rhabdomyosarcoma occurring in children. The tumor arises from organs with a mucosal epithelial surface. It is characterized by the formation of a cambium layer in the affected tissue and polypoid nodules within an abundant myxoid stroma.

Also known as botryoid rhabdomyosarcoma of childhood, childhood botryoid-type embryonal rhabdomyosarcoma, childhood sarcoma Botryoides, paediatric botryoid rhabdomyosarcoma, pediatric botryoid rhabdomyosarcoma — per MONDO

Also identified as

Affected Organs

Organ Involvement Source
Muscle tissue Disease Has Primary Anatomic Site NCIT · CC BY 4.0
Musculature Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Musculoskeletal system Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Striated muscle tissue Disease Has Primary Anatomic Site NCIT · CC BY 4.0