Childhood vagina botryoid rhabdomyosarcoma
Childhood vagina botryoid rhabdomyosarcoma
Definition
A morphologic variant of embryonal rhabdomyosarcoma occurring in female children. The neoplasm arises from the vagina. It is characterized by the formation of a cambium layer in the affected tissue and polypoid nodules with an abundant myxoid stroma.
Also known as botryoid-type embryonal rhabdomyosarcoma of the vagina of childhood, childhood botryoid-type embryonal rhabdomyosarcoma of the vagina, childhood sarcoma Botryoides of the vagina, paediatric botryoid-type embryonal rhabdomyosarcoma of the vagina, pediatric botryoid-type embryonal rhabdomyosarcoma of the vagina, vaginal childhood botryoid-type embryonal rhabdomyosarcoma, vaginal childhood sarcoma Botryoides — per MONDO
Also identified as
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Female reproductive system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Genitourinary system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Muscle tissue | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Musculature | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Musculoskeletal system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Reproductive system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Skeletal muscle | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Skeletal muscle | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Striated muscle tissue | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Vagina | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Vagina | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |