Peripheral epithelioid sarcoma
Peripheral epithelioid sarcoma
Definition
An epithelioid sarcoma involving the extremities. It usually presents as nodular masses in the dermis and subcutaneous tissues or in the tendons and fascia. It frequently recurs and metastasizes to other anatomic sites. The most common sites of metastasis are the lungs, lymph nodes, bones, and brain.
Also known as conventional epithelioid sarcoma, distal-type epithelioid sarcoma — per MONDO