Malignant melanocytic peripheral nerve sheath tumor of mediastinum
Malignant melanocytic peripheral nerve sheath tumor of mediastinum
Definition
A rare variant of malignant peripheral nerve sheath tumor that arises from the mediastinum. It is characterized by the presence of malignant cells that contain melanin.
Also known as malignant mediastinal melanocytic peripheral nerve sheath tumor, malignant mediastinal melanocytic peripheral nerve sheath tumour, malignant melanocytic neoplasm of the peripheral nerve sheath of mediastinum, malignant melanocytic peripheral nerve sheath tumor of mediastinum, malignant melanotic peripheral nerve sheath tumor of the mediastinum, malignant melanotic peripheral nerve sheath tumour of the mediastinum, mediastinal melanocytic MPNST, mediastinum malignant melanocytic neoplasm of the peripheral nerve sheath — per MONDO
Also identified as
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Nerve | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Nervous system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Peripheral nervous system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Peripheral nervous system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Respiratory system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |