Pulmonary artery leiomyosarcoma
Pulmonary artery leiomyosarcoma
Definition
An aggressive malignant smooth muscle neoplasm, arising from the pulmonary artery It is characterized by a proliferation of neoplastic spindle cells.
Also known as leiomyosarcoma of pulmonary artery, leiomyosarcoma of the pulmonary artery, pulmonary artery leiomyosarcoma — per MONDO
Also identified as
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Blood vessel | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Muscle tissue | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Musculature | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Musculoskeletal system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Pulmonary artery | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Smooth muscle | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |