Proximal-type epithelioid sarcoma
Proximal-type epithelioid sarcoma
Definition
An epithelioid sarcoma predominantly involving the pelvis, perineum, and genital organs. It tends to have a more aggressive clinical course as compared to the more frequently seen distal-type epithelioid sarcoma.
Also known as central epithelioid sarcoma, proximal-type epithelioid sarcoma — per MONDO