Autosomal dominant polycystic liver disease
ICD-10 Code
Q44.6
Autosomal dominant polycystic liver disease
Definition
An autosomal dominant inherited condition characterized by many cysts of various sizes scattered throughout the liver.
Also known as AD polycystic liver disease, ADPLD, isolated congenital polycystic liver disease, isolated polycystic liver disease, PCLD, polycystic liver disease — per MONDO
Also identified as
- DOID 0050770 per MONDO
- ICD10CM Q44.6 per MONDO
- ICD9 751.62 per MONDO
- NCIT C82833 per MONDO
- Orphanet 2924 per MONDO
- SCTID 72925005 per MONDO
- UMLS C0158683 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Alimentary part of gastrointestinal system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Alimentary part of gastrointestinal system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Liver | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Liver | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |