Paraganglioma
Paraganglioma
Definition
A benign or malignant neoplasm arising from paraganglia located along the sympathetic or parasympathetic nerves. Infrequently, it may arise outside the usual distribution of the sympathetic and parasympathetic paraganglia. Tumors arising from the adrenal gland medulla are called pheochromocytomas. Morphologically, paragangliomas usually display a nesting (Zellballen) growth pattern. There are no reliable morphologic criteria to distinguish between benign and malignant paragangliomas. The only definitive indicator of malignancy is the presence of regional or distant metastases.
Also known as neoplasm of paraganglion, neoplasm of the paraganglion, paraganglioma, paragangliomas, paraganglion neoplasm, paraganglion tumor, paraganglion tumour, Paraganglionic neoplasm, Paraganglionic tumor, Paraganglionic tumour, tumor of paraganglion, tumor of the paraganglion, tumour of paraganglion, tumour of the paraganglion — per MONDO
Also identified as
- DOID 0050773 per MONDO
- ICD9 239.7 per MONDO
- MESH D010235 per MONDO
- NCIT C3308 per MONDO
- SCTID 127027008 per MONDO
- UMLS C0030421 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Autonomic nervous system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Endocrine gland | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Endocrine gland | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Nervous system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Peripheral nervous system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |