Adrenal gland pheochromocytoma
Adrenal gland pheochromocytoma
Definition
A benign or malignant neuroendocrine neoplasm of the sympathetic nervous system that secretes catecholamines. It arises from the chromaffin cells of the adrenal medulla. Clinical presentation includes headaches, palpitations, chest and abdominal pain, hypertension, fever, and tremor. Microscopically, a characteristic nesting (zellballen) growth pattern is usually seen. Other growth patterns including trabecular pattern may also be present.
Also known as adrenal gland chromaffin paraganglioma, adrenal gland Chromaffinoma, adrenal gland paraganglioma, adrenal gland pheochromocytoma, adrenal medullary paraganglioma, adrenal medullary pheochromocytoma, adrenal pheochromocytoma, chromaffin paraganglioma of the adrenal gland, Intraadrenal paraganglioma, PCC, pheochromocytoma (adrenal) — per MONDO
Also identified as
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Adrenal glands | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Adrenal glands | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Autonomic nervous system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Endocrine gland | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Endocrine gland | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Nervous system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Peripheral nervous system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Sympathetic nervous system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |