Clear cell sarcoma of kidney

Clear cell sarcoma of kidney

Definition

A rare pediatric sarcoma affecting the kidney. It is characterized by the presence of epithelioid or spindle cells forming cords or nests, separated by fibrovascular septa. It is associated with internal tandem duplications in the BCOR gene. It metastasizes to lung, bone, brain and soft tissue.

Also known as CCSK, childhood clear cell sarcoma of the kidney, childhood kidney clear cell sarcoma, childhood renal clear cell sarcoma, clear cell sarcoma - kidney, clear cell sarcoma of kidney, clear cell sarcoma of the kidney, kidney clear cell sarcoma, paediatric kidney clear cell sarcoma, paediatric renal clear cell sarcoma, pediatric kidney clear cell sarcoma, pediatric renal clear cell sarcoma, renal clear cell sarcoma — per MONDO

Also identified as

Affected Organs

Organ Involvement Source
Adult mammalian kidney Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Adult mammalian kidney Disease Has Primary Anatomic Site NCIT · CC BY 4.0
Genitourinary system Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Renal system Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Upper urinary tract Disease Has Associated Anatomic Site NCIT · CC BY 4.0