Ganglioneuroma
Ganglioneuroma
Definition
A benign neuroblastic tumor of the sympathetic nervous system that occurs in childhood. Ganglioneuroma typically arises from the sympathetic trunk in the mediastinum. Histologic features include spindle cell proliferation (resembling a neurofibroma) and the presence of large ganglion cells. Common presenting features include a palpable abdominal mass, hepatomegaly, and a thoracic mass detected on routine chest X-ray.
Also known as ganglioneuroma, ganglioneuroma (disease), ganglioneuroma (Schwannian Stroma-dominant), ganglioneuroma, benign, neural Crest tumor, benign — per MONDO
Also identified as
- DOID 4817 per MONDO
- ICD9 215.9 per MONDO
- NCIT C3049 per MONDO
- Orphanet 251992 per MONDO
- SCTID 116371000119107 per MONDO
- UMLS C0017075 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Autonomic nervous system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Nervous system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Nervous system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Peripheral nervous system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Peripheral nervous system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |