Extra-adrenal sympathetic paraganglioma
Extra-adrenal sympathetic paraganglioma
Definition
A benign or malignant sympathetic paraganglioma arising from paraganglia outside the adrenal gland. Clinical symptoms are related to secretion of catecholamines. Representative examples include the superior and inferior paraaortic and bladder paragangliomas.
Also known as extra-adrenal chromaffin neoplasm, extra-adrenal Chromaffinoma, extra-adrenal pheochromocytoma, extra-adrenal sympathetic paraganglioma, extra-adrenal sympathetic Paraganglionic neoplasm, extraadrenal pheochromocytoma — per MONDO
Also identified as
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Autonomic nervous system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Endocrine gland | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Endocrine gland | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Nervous system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Peripheral nervous system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Sympathetic nervous system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |