Dysembryoplastic neuroepithelial tumor
Dysembryoplastic neuroepithelial tumor
Definition
A benign glial-neuronal neoplasm. It is usually supratentorial, located, generally, in the cortex and occurs in children and young adults with a long-standing history of partial seizures. A histologic hallmark of this tumor is the 'specific glioneuronal element', characterized by columns, made up of bundles of axons, oriented perpendicularly to the cortical surface.B
Also known as DNET, DNT, dysembryoplastic neuroepithelial neoplasm, dysembryoplastic neuroepithelial tumor (morphologic abnormality), dysembryoplastic neuroepithelial tumour (morphologic abnormality) — per MONDO
Also identified as
- DOID 2679 per MONDO
- NCIT C9505 per MONDO
- Orphanet 251946 per MONDO
- SCTID 87211000119104 per MONDO
- UMLS C1266177 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Brain | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Brain | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Central nervous system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Central nervous system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Cerebral cortex | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Nervous system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |