Cerebral amyloid angiopathy

ICD-10 Code I68.0

Cerebral amyloid angiopathy

Definition

Hereditary cerebral hemorrhage with amyloidosis (HCHWA) describes a group of rare familial central nervous system disorders characterized by amyloid deposition in the cerebral blood vessels leading to hemorrhagic and non-hemorrhagic strokes, focal neurological deficits, and progressive cognitive decline eventually leading to dementia.

Also known as dutch hereditary cerebral amyloid angiopathy, HCHWA, hereditary cerebral haemorrhage with amyloidosis - Dutch type, hereditary cerebral hemorrhage with amyloidosis - Dutch type — per MONDO

Also identified as

Affected Organs

Organ Involvement Source
Brain Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Brain Disease Has Primary Anatomic Site NCIT · CC BY 4.0
Cardiovascular system Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Cardiovascular system Disease Has Primary Anatomic Site NCIT · CC BY 4.0
Central nervous system Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Central nervous system Disease Has Primary Anatomic Site NCIT · CC BY 4.0
Nervous system Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Nervous system Disease Has Primary Anatomic Site NCIT · CC BY 4.0