Lipoatrophic diabetes

Lipoatrophic diabetes

Definition

A rare syndrome characterized by almost complete absence of body fat, accentuated muscularity, insulin-resistant diabetes, hyperlipidemia, hepatomegaly, and hypermetabolism.

Also known as diabete, lipoatrophic, lipoatrophic diabetes — per MONDO

Also identified as

Affected Organs

Organ Involvement Source
Alimentary part of gastrointestinal system Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Alimentary part of gastrointestinal system Disease Has Primary Anatomic Site NCIT · CC BY 4.0
Endocrine gland Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Pancreas Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Pancreas Disease Has Primary Anatomic Site NCIT · CC BY 4.0