Lung lymphangioleiomyomatosis
Lung lymphangioleiomyomatosis
Definition
Lymphangiomyomatosis involving the lungs and local lymph nodes. Patients usually present with chylous pleural effusion. The clinical course is variable. Patients with resectable lesions usually have a favorable clinical outcome. Patients with diffuse lesions usually have a progressive clinical course.
Also known as lung lymphangioleiomyomatosis, lung lymphangiomyomatosis — per MONDO
Also identified as
- DOID 3319 per MONDO
- ICD9 518.89 per MONDO
- NCIT C38153 per MONDO
- Orphanet 538 per MONDO
- SCTID 277844007 per MONDO
- UMLS C0349649 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Lungs | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Lungs | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Respiratory system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |