Malignant adrenal gland pheochromocytoma
Malignant adrenal gland pheochromocytoma
Definition
A pheochromocytoma that metastasizes to other anatomic sites. Common sites of metastasis include lymph nodes, bones, liver, and lung. Morphologic features associated with malignant pheochromocytomas include: atypical mitotic figures, capsular and vascular invasion, tumor cell necrosis, and high mitotic activity.
Also known as adrenal gland pheochromocytoma, malignant, malignant adrenal gland chromaffin neoplasm, malignant adrenal gland chromaffin paraganglioma, malignant adrenal gland chromaffin tumor, malignant adrenal gland chromaffin tumour, malignant adrenal gland Chromaffinoma, malignant adrenal gland paraganglioma, malignant adrenal gland pheochromocytoma, malignant adrenal medullary paraganglioma, malignant adrenal medullary pheochromocytoma, malignant adrenal pheochromocytoma, malignant pheochromocytoma, pheochromoblastoma, pheochromocytoma, malignant — per MONDO
Also identified as
- DOID 0080347 per MONDO
- NCIT C4220 per MONDO
- SCTID 21851000119103 per MONDO
- UMLS C0334419 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Adrenal glands | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Adrenal glands | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Autonomic nervous system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Endocrine gland | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Endocrine gland | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Nervous system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Peripheral nervous system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Peripheral nervous system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Sympathetic nervous system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |