Paranasal sinus adenoid cystic carcinoma

Paranasal sinus adenoid cystic carcinoma

Definition

A rare adenoid cystic carcinoma that arises from the paranasal sinuses. It usually has an aggressive clinical course characterized by high recurrence rates and distant metastases.

Also known as accessory sinus adenoid cystic carcinoma, adenoid cystic carcinoma of accessory sinus, adenoid cystic carcinoma of paranasal sinus, adenoid cystic carcinoma of the accessory sinus, adenoid cystic carcinoma of the paranasal sinus, paranasal sinus adenoid cystic carcinoma — per MONDO

Also identified as

Affected Organs

Organ Involvement Source
Craniocervical region Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Craniocervical region Disease Has Primary Anatomic Site NCIT · CC BY 4.0