Retroperitoneal inflammatory myofibroblastic tumor
Retroperitoneal inflammatory myofibroblastic tumor
Definition
A multinodular intermediate fibroblastic neoplasm arising from the retroperitoneum. It is characterized by the presence of spindle-shaped fibroblasts and myofibroblasts, and a chronic inflammatory infiltrate composed of eosinophils, lymphocytes and plasma cells.
Also known as retroperitoneal inflammatory myofibroblastic tumor, retroperitoneal space inflammatory myofibroblastic tumor, retroperitoneal space inflammatory myofibroblastic tumour — per MONDO