Small intestinal enteropathy-associated T-cell lymphoma
Small intestinal enteropathy-associated T-cell lymphoma
Definition
An enteropathy-associated T-cell lymphoma arising from the small intestine, most commonly the jejunum or ileum. Patients usually present with abdominal pain, often associated with intestinal perforation. There is often a history of celiac disease. The lymphoma cells are usually medium-sized to large and form an ulcerating mucosal lesion with invasion of the small intestinal wall. Villous atrophy is present in the adjacent small intestinal mucosa. In a minority of cases the lymphoma cells are medium-sized and form a monomorphic infiltrate.
Also known as enteropathy-associated T-cell lymphoma of small intestine, small intestinal EATL, small intestinal enteropathy-type T-cell lymphoma, small intestine enteropathy-associated T-cell lymphoma — per MONDO
Also identified as
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Alimentary part of gastrointestinal system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Alimentary part of gastrointestinal system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Intestine | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Intestine | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Lymphoid system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Small intestine | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Small intestine | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |