Adrenal cortex carcinoma

Adrenal cortex carcinoma

Definition

A rare, usually large (greater than 5cm), malignant epithelial tumor arising from the adrenal cortical cells. Symptoms are usually related to the excessive production of hormones, and include Cushing's syndrome and virilism in women. Common sites of metastasis include liver, lung, bone, and retroperitoneal lymph nodes. Advanced radiologic procedures have enabled the detection of small tumors, resulting in the improvement of the 5-year survival.

Also known as ACC, adenocarcinoma, adrenocortical, malignant, adrenal cortex adenocarcinoma, adrenal cortex carcinoma, adrenal cortical adenocarcinoma, adrenal cortical carcinoma, adrenal cortical carcinoma (morphologic abnormality), adrenocortical carcinoma, adrenocortical carcinoma (disease), carcinoma of adrenal cortex, carcinoma of the adrenal cortex, carcinoma, adrenocortical, malignant, cortical cell carcinoma — per MONDO

Also identified as

Affected Organs

Organ Involvement Source
Adrenal glands Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Adrenal glands Disease Has Primary Anatomic Site NCIT · CC BY 4.0
Endocrine gland Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Endocrine gland Disease Has Primary Anatomic Site NCIT · CC BY 4.0