Adrenal cortex carcinoma
Adrenal cortex carcinoma
Definition
A rare, usually large (greater than 5cm), malignant epithelial tumor arising from the adrenal cortical cells. Symptoms are usually related to the excessive production of hormones, and include Cushing's syndrome and virilism in women. Common sites of metastasis include liver, lung, bone, and retroperitoneal lymph nodes. Advanced radiologic procedures have enabled the detection of small tumors, resulting in the improvement of the 5-year survival.
Also known as ACC, adenocarcinoma, adrenocortical, malignant, adrenal cortex adenocarcinoma, adrenal cortex carcinoma, adrenal cortical adenocarcinoma, adrenal cortical carcinoma, adrenal cortical carcinoma (morphologic abnormality), adrenocortical carcinoma, adrenocortical carcinoma (disease), carcinoma of adrenal cortex, carcinoma of the adrenal cortex, carcinoma, adrenocortical, malignant, cortical cell carcinoma — per MONDO
Also identified as
- DOID 3948 per MONDO
- DOID 3959 per MONDO
- DOID 660 per MONDO
- NCIT C9325 per MONDO
- Orphanet 1501 per MONDO
- SCTID 255035007 per MONDO
- UMLS C0206686 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Adrenal glands | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Adrenal glands | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Endocrine gland | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Endocrine gland | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |