Lymphangiomyoma
Lymphangiomyoma
Definition
A neoplasm with perivascular epithelioid cell differentiation, often associated with tuberous sclerosis. It is characterized by the presence of smooth muscle and epithelioid cells and by the proliferation of lymphatic vessels. Sites of involvement include the lymph nodes, lung, mediastinum, and retroperitoneum.
Also known as lymphangioleiomyoma, lymphangiomyoma — per MONDO
Also identified as
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Lymphatic vessels | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |