Somatostatinoma

Definition

A rare, usually malignant neuroendocrine tumor arizing from delta cells. This neoplasm produces large amounts of somatostatin, which may result in a syndrome characterized by diarrhea, steatorrhea, weight loss, and gastric hyposecretion. Sixty percent are found in the pancreas and 40% in the duodenum or jejunum. The peak incidence occurs between 40 and 60 years of age; women are affected more than men by 2:1.

Also known as Delta cell tumor, Delta cell tumour, somatostatin cell tumor, somatostatin producing tumor, somatostatin producing tumour, somatostatin-producing NET, somatostatin-producing neuroendocrine tumor, somatostatin-producing neuroendocrine tumour, somatostatin-producing tumor, somatostatin-producing tumour, somatostatinoma, tumor of Delta cells, tumor of the Delta cells, tumour of Delta cells, tumour of the Delta cells — per MONDO

Also identified as

• DOID 4430 per MONDO
• ICD9 235.5 per MONDO
• MESH D013005 per MONDO
• NCIT C3379 per MONDO
• Orphanet 97283 per MONDO
• SCTID 253006001 per MONDO
• UMLS C0037661 per MONDO

Affected Organs