Glucocorticoid-remediable aldosteronism
ICD-10 Code
E26.02
Glucocorticoid-remediable aldosteronism
Definition
Familial hyperaldosteronism type I (FH-I) is a rare heritable, glucocorticoid remediable form of primary aldosteronism (PA) characterized by early-onset hypertension, hyperaldosteronism, variable hypokalemia, low plasma renin activity (PRA), and abnormal production of 18-oxocortisol and 18-hydroxycortisol.
Also known as aldosteronism, glucocorticoid-remediable, dexamethasone-sensitive hypertension, familial hyperaldosteronism type 1, FH-I, FH1, glucocorticoid-remediable aldosteronism, glucocorticoid-sensitive hypertension, GRA — per MONDO