Congenital total pulmonary venous return anomaly
Congenital total pulmonary venous return anomaly
Definition
Total pulmonary venous return (TAPVR) is a form of congenital pulmonary venous return where all of the pulmonary veins drain into the right atrium or one of its tributaries, instead of the left atrium, leading to various manifestations such as fatigue, exertional dyspnea, pulmonary arterial hypertension, cyanosis and progressive congestive heart failure.
Also known as TAPVR, total anomalous pulmonary venous return — per MONDO
Also identified as
- DOID 4297 per MONDO
- ICD9 747.41 per MONDO
- NCIT C98585 per MONDO
- OMIM 106700 per MONDO
- Orphanet 99125 per MONDO
- SCTID 111323005 per MONDO
- UMLS C4551903 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Cardiovascular system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Cardiovascular system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |