Nevoid basal cell carcinoma syndrome
Nevoid basal cell carcinoma syndrome
Definition
A rare hereditary disorder due to autosomal dominant transmission with hamartosis characterized by multiple early-onset basal cell carcinoma (BCC), multiple jaw keratocysts and skeletal abnormalities.
Also known as basal cell nevus syndrome, Gorlin syndrome, Gorlin-Goltz syndrome, multiple basal cell carcinomas, NBCCS, nevoid basal cell cancer syndrome, nevoid basal cell carcinoma syndrome — per MONDO