Self-limited epilepsy with centrotemporal spikes

Definition

A childhood-onset epilepsy syndrome that is characterized by onset of seizures between 3 and 14 years (peak 8-9 years) that usually resolve by age 13 years, but can occasionally occur up to age 18 years of age. Both sexes are affected. Antecedent, birth and neonatal history is normal. A history of febrile seizure (in 5-15%) may be seen. A history of Panayiotopoulos syndrome may be present in a very small number of cases. Neurological exam and head size is normal. Development and cognition prior to onset of seizures is normal. During the course of the active epilepsy, behavioral and neuropsychological deficits may be found, particularly in language and executive functioning. These deficits improve when seizures remit.

Also known as BCECTS, BECRS, BECTS, benign childhood epilepsy with centrotemporal spikes, benign epilepsy of childhood with centrotemporal spikes, benign epilepsy with centrotemporal spikes, benign familial epilepsy of childhood with rolandic spikes, benign Rolandic epilepsy, benign Rolandic epilepsy (BRE), benign Rolandic epilepsy of childhood (BREC), BRE, centralopathic epilepsy, centrotemporal epilepsy, centrotemporal epilepsy, isolated cases, childhood epilepsy with centrotemporal spikes, Rolandic epilepsy, temporal-central focal epilepsy — per MONDO

Also identified as

• DOID 3329 per MONDO
• ICD9 345.80 per MONDO
• NCIT C116538 per MONDO
• OMIM 117100 per MONDO
• Orphanet 1945 per MONDO
• SCTID 44145005 per MONDO
• UMLS C0376532 per MONDO

Affected Organs