Charcot-Marie-Tooth disease type 1B
Charcot-Marie-Tooth disease type 1B
Definition
A sensorineural peripheral polyneuropathy affecting approximately 1 in 2,500 individuals, and is the most common inherited disorder of the peripheral nervous system. Autosomal dominant, autosomal recessive, and X-linked forms have been recognized.
Also known as Charcot-Marie-Tooth disease type 1 caused by mutation in MPZ, Charcot-Marie-Tooth disease, type 1B, CMT1B, HMSN IB, HMSN1B, MPZ Charcot-Marie-Tooth disease type 1 — per MONDO
Also identified as
- DOID 0110152 per MONDO
- NCIT C118782 per MONDO
- OMIM 118200 per MONDO
- Orphanet 101082 per MONDO
- UMLS C0270912 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Musculature | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Musculature | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Musculoskeletal system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Musculoskeletal system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Nervous system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Nervous system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Peripheral nervous system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Peripheral nervous system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |