Dentin dysplasia-sclerotic bones syndrome

Dentin dysplasia-sclerotic bones syndrome

Definition

A rare, genetic odontologic disease characterized by the clinical, radiographic, and histologic features of dentine dysplasia and osteosclerosis of all long bones, with heavy cortical bone and narrowed or occluded marrow spaces. There have been no further descriptions in the literature since 1977.

Also identified as