Dentinogenesis imperfecta type 2

Definition

Dentinogenesis imperfecta type 2 (DGI-2) is a rare, severe form of dentinogenesis imperfecta (DGI) and is characterized by weakness and discoloration of all teeth.

Also known as Capdepont teeth, dentinogenesis imperfecta type 1, dentinogenesis imperfecta, Shields type 2, dentinogenesis imperfecta, Shields type II, DGI-2, DI-2 — per MONDO

Also identified as

• OMIM 125490 per MONDO
• Orphanet 166260 per MONDO
• UMLS C2973527 per MONDO