Epidermolysis bullosa simplex 1B, generalized intermediate
Epidermolysis bullosa simplex 1B, generalized intermediate
Definition
Non-Dowling-Meara generalized epidermolysis bullosa simplex, formerly known as epidermolysis bullosa simplex, Kobner type (EBS-K) is a generalized basal subtype of epidermolysis bullosa simplex (EBS) characterized by non-herpetiform blisters and erosions arising in particular at sites of friction.
Also known as EBS, generalised intermediate, EBS, generalized intermediate, epidermolysis bullosa simplex 1B, generalized intermediate, epidermolysis bullosa simplex, Kobner type, epidermolysis bullosa simplex, Koebner type, generalised EBS, non-Dowling-Meara type, generalised epidermolysis bullosa simplex, non-Dowling-Meara type, generalized EBS, non-Dowling-Meara type, generalized epidermolysis bullosa simplex, non-Dowling-Meara type — per MONDO