Epidermolysis bullosa simplex 5A, Ogna type
Epidermolysis bullosa simplex 5A, Ogna type
Definition
A basal subtype of epidermolysis bullosa simplex (EBS) characterized by sometimes widespread, primarily acral blistering.
Also known as EBSOG, epidermolysis bullosa simplex 5A, Ogna type, epidermolysis bullosa simplex, Ogna type — per MONDO