Pilomatrixoma
Pilomatrixoma
Definition
Pilomatrixoma is a rare and benign hair cell-derived tumor occurring mostly in young adults (usually under the age of 20) and characterized as a 3-30 mm solitary, painless, firm, mobile, deep dermal or subcutaneous tumor, most commonly found in the head, neck or upper extremities. When superficial, the tumors tint the skin blue-red. Multiple pilomatrixomas are seen in myotonic dystrophy, Gardner syndrome, Rubinstein-Taybi syndrome, and Turner syndrome.
Also known as calcifying Epitherlioma of Malherbe, epithelioma calcificans of Malherbe, pilomatricoma, pilomatricoma, somatic, pilomatrixoma, pilomatrixoma, benign — per MONDO
Also identified as
- DOID 5374 per MONDO
- MESH D018296 per MONDO
- NCIT C7368 per MONDO
- OMIM 132600 per MONDO
- Orphanet 91414 per MONDO
- SCTID 274901004 per MONDO
- UMLS C0206711 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Exocrine system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Hair | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Hair follicles | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Integumental system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Skin of body | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Skin of body | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |