Hypotrichosis-lymphedema-telangiectasia syndrome (grouping)
Hypotrichosis-lymphedema-telangiectasia syndrome (grouping)
Definition
Hypotrichosis - lymphedema - telangiectasia is an extremely rare syndromic lymphedema disorder characterized by early-onset hypotrichosis, childhood-onset lymphedema, and variable telangiectasia, particularly of the palms.
Also identified as
- Orphanet 69735 per MONDO