Kasabach-Merritt syndrome

Definition

Kasabach-Merritt syndrome (KMS), also known as hemangioma-thrombocytopenia syndrome, is a rare disorder characterized by profound thrombocytopenia, microangiopathic hemolytic anemia, and subsequent consumptive coagulopathy in association with vascular tumors, particularly kaposiform hemangioendothelioma or tufted angioma.

Also known as hemangioma-hemorrhage syndrome, hemangioma-thrombocytopenia syndrome, hemangiomatosis with thrombocytopenia, Kasabach Merritt phenomenon, Kasabach Merritt syndrome, Kasabach-Merritt Phenomenon, Kasabach-Merritt syndrome, thrombocytopenia-hemangioma syndrome, thrombopenia-hemangioma syndrome — per MONDO

Also identified as

• ICD9 287.39 per MONDO
• MESH D059885 per MONDO
• NCIT C3821 per MONDO
• OMIM 141000 per MONDO
• Orphanet 2330 per MONDO
• SCTID 86635005 per MONDO
• UMLS C0221025 per MONDO

Affected Organs