TNF receptor 1-associated periodic fever syndrome
TNF receptor 1-associated periodic fever syndrome
Definition
A periodic fever syndrome, characterized by recurrent fever, arthralgia, myalgia and tender skin lesions lasting for 1 to 3 weeks, associated with skin, joint, ocular and serosal inflammation and complicated by secondary amyloidosis.
Also known as familial Hibernian fever, FHF, Hibernian fever, familial, TNF receptor 1-associated periodic fever syndrome, TNF receptor 1-associated periodic syndrome, TNF receptor-associated periodic syndrome, TRAPS, TRAPS syndrome, tumor necrosis factor receptor 1 associated periodic syndrome, tumor necrosis factor receptor 1-associated periodic syndrome, Tumor Necrosis Factor Receptor-Associated Periodic Syndrome, tumour necrosis factor receptor 1 associated periodic syndrome, tumour necrosis factor receptor 1-associated periodic syndrome, tumour necrosis factor receptor-associated periodic syndrome — per MONDO