Familial generalized lentiginosis
Familial generalized lentiginosis
Definition
Familial generalized lentiginosis is a rare, inherited, skin hyperpigmentation disorder characterized by widespread lentigines without associated noncutaneous abnormalities. Patients present multiple brown to dark brown, non-elevated macula of 0.2 to 1 cm in diameter, spread over the entire body, sometimes including palms or soles, but never oral mucosa.
Also known as familial lentigines profusa, familial multiple lentigines syndrome without systemic involvement — per MONDO