Cystoid macular edema
Cystoid macular edema
Definition
An autosomal dominantly inherited cystoid macular edema manifesting with macular atrophy, strabismus and, sometimes, pericentral retinitis pigmentosa. It is associated with a poor visual prognosis.
Also known as autosomal dominant cystoid macular edema, autosomal dominant cystoid macular oedema, DCMD, familial macular edema, familial macular oedema — per MONDO
Also identified as
- DOID 4447 per MONDO
- NCIT C34794 per MONDO
- OMIM 153880 per MONDO
- Orphanet 75381 per MONDO
- SCTID 312921000 per MONDO
- UMLS C0024440 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Camera-type eye | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Camera-type eye | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Retina | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Retina | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |