Melkersson-Rosenthal syndrome
ICD-10 Code
G51.2
Melkersson-Rosenthal syndrome
Definition
The Melkersson-Rosenthal syndrome is a rare disorder characterized by a triad of recurrent orofacial swelling, relapsing facial paralysis and fissured tongue and onset in childhood or early adolescence. It has an estimated incidence of 8/10,000. The etiology is unknown but hereditary predisposition is suspected.
Also known as Melkersson-Rosenthal syndrome, Melkersson's syndrome — per MONDO