Linear nevus sebaceous syndrome
Linear nevus sebaceous syndrome
Definition
Linear nevus sebaceous syndrome (LNSS) is characterized by the association of a large sebaceous nevus, usually appearing on the face or on the scalp, with a broad spectrum of abnormalities that may affect every organ system, including the central nervous system (brain neoplasms, hemimegalencephaly and lateral ventricle enlargement).
Also known as linear sebaceous Nevus, Nevus sebaceous of Jadassohn, Nevus sebaceus of Jadassohn, Nevus Sebaceus Syndrome, organoid Nevus, organoid nevus syndrome, Schimmelpenning syndrome, Schimmelpenning-Feuerstein-Mims syndrome, somatic mosaic, Solomon syndrome — per MONDO