Ocular cicatricial pemphigoid

Definition

Ocular cicatricial pemphigoid (OCP) is a form of mucous membrane pemphigoid (a group of rare, chronic autoimmune disorders) that affects the eyes. In the early stages, people with OCPgenerally experience chronic or relapsing conjunctivitis that is often characterized by tearing, irritation, burning, and/or mucus drainage. If left untreated, OCP can progress to severe conjunctiva scarring and vision loss. Involvement of other mucosal sites and the skin may also occur in OCP. The exact underlying cause is currently unknown. The treatment of OCP aims to slow disease progression and prevent complications. This usually involves long-term use of medications called immunomodulators which help regulate or normalize the immune system.

Also known as ocular cicatricial pemphigoid, ocular pemphigoid — per MONDO

Also identified as

• NCIT C84939 per MONDO
• OMIM 164185 per MONDO
• Orphanet 99922 per MONDO
• SCTID 314757003 per MONDO
• SCTID 34250006 per MONDO
• UMLS C1282359 per MONDO

Affected Organs